CLINICAL CASE OF TUBEROUS SCLEROSIS AND DIAGNOSTIC POSSIBILITIES OF OPTICAL COHERENT TOMOGRAPHY AND ANGIOGRAPHY

Objective(s). The aim is to determine the possibilities of optical coherence tomography (OCT), angiography (OCTA) eye in diagnosis tuberous sclerosis and assess dynamics this rare pathological process.
 Methods. clinical case a 19-year-old patient with involvement process visual organ presented. Ophthalmological examination also related specialists are carried out. Visual acuity was right 1.0 left correction. One focus detected on during ophthalmoscopy. Two focuses were revealed eye. OCT OCTA performed device Optovue RTVue 100 XR Avanti (Optovue Inc, USA). analyzed different modes. Automatic manual segmentation used analysis.
 Results. retina allowed visualize homogeneous formations at level inner layers neuroepithelium areas by ophthalmoscopy, exclude from vitreous choroid. foci had clear boundaries protruded into vitreous. retinal under dislocated thinned, but structure all clearly visible. Manual showed change location large vessels superficial plexus growth abnormal vessels. Differential retinoblastoma inflammatory diseases, such as chorioretinitis. Confirmation type phacomatosis obtained other organs. 4 primary signs 2 secondary sclerosis.
 Conclusion. use segment choroid, localize detect hamartoma. Identified combination ophthalmic manifestations (presence hamartomas) made it possible establish diagnosis.